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Denys-Drash syndrome


    This 3-year-old female was diagnosed of Denys-Drash syndrome and underwent bilateral nephrectomy because of bilateral Wilms’ tumor. (Fig 1) She received temporary hemodialysis before permanent peritoneal dialysis was initiated. She was regularly followed-up at our pediatric nephrology clinic and was surveilled under special dialysis nurses, dietitians and social workers. Currently, she underwent continuous cyclic peritoneal dialysis for three years without any eventful complications.

    Art editor Img

    Fig. 1 Bilateral Wilms’ tumor presenting with enlarged kidneys and end stage kidney disease. The normal kidney (Arrow) was compressed with the malignancy. (Arrowhead)