This 3-year-old female was diagnosed of Denys-Drash syndrome and underwent bilateral nephrectomy because of bilateral Wilms’ tumor. (Fig 1) She received temporary hemodialysis before permanent peritoneal dialysis was initiated. She was regularly followed-up at our pediatric nephrology clinic and was surveilled under special dialysis nurses, dietitians and social workers. Currently, she underwent continuous cyclic peritoneal dialysis for three years without any eventful complications.
Fig. 1 Bilateral Wilms’ tumor presenting with enlarged kidneys and end stage kidney disease. The normal kidney (Arrow) was compressed with the malignancy. (Arrowhead)